An Atypical Case of POEMS Syndrome Associated with Autonomic Dysfunction
作者: Mariana B. HämmerleKarina L. PiresMárcia B. HammerlePedro de Mello Vianna P. GalvãoLavinia L. BergierVitor V.Monique de França SilvaMarcelo R. CaetanoFelix PerezKevin A. ReyesCamila B. AlmenaraLarissa Cristine de Souza LopesDaiane V. Botelho
刊名: The Open Neurology Journal, 2019, Vol.13 , pp.92-95
来源数据库: Bentham OA
DOI: 10.2174/1874205X01913010092
关键词: POEMSCow-FukaseTakatsukiPolyneuropathyDysautonomiaCastleman disease
原始语种摘要: A 52 year old patient showed, for two years, symptoms compatible with sensorimotor polyneuropathy preventing him from walking. An electroneuromyography found a demyelinating pattern suggesting Chronic Inflammatory Demyelinating Polyneuropathy (CIDP). The patient did not respond to corticosteroid therapy and later suffered sexual Dysfunction, Swelling, Lymphadenopathy, Hypotension, astrointestinal dysmotility, urinary retention and neuropathic pain. Analysis of the Cerebrospinal Fluid (CSF) revealed elevated protein levels and Computed Tomography (CT) scan found sclerotic bone lesions. High Vascular Endothelial Growth Factor (VEGF) levels and the results of Lambda light-Chain monoclonal gammopathy in urine protein Electrophoresis Suggested a Diagnosis of POEMS syndrome. The most striking...
全文获取路径: Bentham 

  • polyneuropathy 多神经病
  • corticosteroid 皮质甾类
  • sclerotic 硬化的
  • atypical 非典型的
  • protein 蛋白质
  • dysautonomia 家族性自竹经机能异常
  • found 创立
  • neuropathic 神经病的
  • sensorimotor 感觉运动的
  • monoclonal 单细胞系的