Management and long-term outcomes of sarcoidosis-associated pulmonary hypertension
作者: Athénaïs BouclyVincent CottinHilario NunesXavier JaïsAbdelatif TaziGrégoire PrévôtMartine Reynaud-GaubertClaire DromerCatherine ViacrozeDelphine Horeau-LanglardChristophe PisonEmmanuel BergotJulie TracletJason WeatheraldGérald SimonneauDominique ValeyreDavid MontaniMarc HumbertOlivier SitbonLaurent Savale
作者单位: 1Université Paris-Sud, Faculté de Médecine, Université Paris-Saclay, Le Kremlin-Bicêtre, France
2Service de Pneumologie, AP-HP, Centre de Référence de l'Hypertension Pulmonaire, Hôpital Bicêtre, Le Kremlin-Bicêtre, France
3INSERM UMR_S 999, Hôpital Marie Lannelongue, Le Plessis Robinson, France
4Université Lyon-1, HCL, Service de Pneumologie, Centre de Référence des Maladies Pulmonaires Rares, Hôpital Louis Pradel, Lyon, France
5Service de Pneumologie, AP-HP, Hôpital Avicenne, Université Paris 13, Bobigny, France
6Service de Pneumologie, AP-HP, Hôpital Saint-Louis, Université Paris-Diderot, Paris, France
7Service de Pneumologie, CHU de Toulouse, Hôpital Larrey, Toulouse, France
8Service de Pneumologie, CHU Nord, Aix-Marseille Université, Marseille, France
9Service de Maladies Respiratoires, CHU de Bordeaux, Hôpital du Haut Lévêque, Université de Bordeaux, Pessac, France
10Service de Pneumologie, CHU de Rouen, Hôpital Bois-Guillaume, Rouen, France
11Service de Pneumologie, CHU de Nantes, Hôpital Laënnec, Nantes,
刊名: European Respiratory Journal, 2017, Vol.50 (4)
来源数据库: European Respiratory Society
DOI: 10.1183/13993003.00465-2017
原始语种摘要: Studies reporting the effects of modern strategies with pulmonary arterial hypertension (PAH)-targeted therapies in sarcoidosis-associated pulmonary hypertension (S-APH) are limited.(#br)Clinical and haemodynamic data from newly diagnosed patients with severe S-APH (mean pulmonary artery pressure (mPAP) >35 mmHg or mPAP 25–35 mmHg with cardiac index <2.5 L·min−1·m−2) were collected from the French Pulmonary Hypertension Registry between 2004 and 2015.(#br)Data from 126 patients with severe S-APH were analysed (mean± sd age 57.5±11.6 years, 74% radiological stage IV). 97 patients (77%) received PAH-targeted therapy and immunosuppressive therapy was initiated or escalated in 33 patients at the time of pulmonary hypertension diagnosis. Four months after PAH-targeted...
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关键词翻译
关键词翻译
  • pulmonary 肺的
  • hypertension 高血压
  • sarcoidosis 肉样瘤病
  • associated 相关的
  • targeted 对准目标的
  • escalation 逐步升级
  • prognosis 预报
  • exercise 练习
  • improvement 改良
  • PAH Pitch Attitude Hold