Two-Stage Surgical Treatment of Severe Cherubism
作者: Cassio Eduardo Raposo-AmaralMarcelo de Campos GuidiStephen M. WarrenAna Beatriz AlmeidaEliane M. Ingrid AmstaldenValdenize TizianeCassio Menezes Raposo-Amaral
作者单位: 1From the
刊名: Annals of Plastic Surgery, 2007, Vol.58 (6), pp.645-651
来源数据库: Wolters Kluwer Journal
DOI: 10.1097/
原始语种摘要: Cherubism is an autosomal-dominant syndrome characterized by excessive bilateral maxillomandibular bony degeneration followed by fibrous tissue hyperplasia. Eight patients (age, 6–15 years; mean, 11 years) with severe cherubism were treated with a 2-stage operation by the same senior surgeon (C.M.R.-A.) over an 18-year period, 1987 through 2005. Severity was based on a modified Motamedi classification system. The diagnosis was established clinically, radiographically, and histologically. Postoperative follow up ranged from 2 to 18 years (mean, 5.1 years). All patients underwent 2-stage surgical treatment. In the first stage, the anterior wall of the maxilla was osteotomized and removed (n = 5). The cherubic lesion was curetted from the maxilla and orbits. The maxilla was recontoured on...
全文获取路径: Wolters Kluwer 
影响因子:1.384 (2012)

  • cherubism 家族性颌骨增大
  • maxillary 上颌骨
  • curettage 刮除术
  • mandible 下颌
  • ectropion 外翻
  • profoundly 深深地
  • bilateral 双边的
  • clinically 临床上
  • eyelid 
  • throughout 遍及